Wednesday, March 31, 2010 11:59 AM, CDT

Throughout the week we told that it would take time for Elizabeth to get better. It was recommeded that a central line be started in one of her veins to be able to get her medication in to her system without having to have numerous IV's so that was started sometime during the week. Elizabeth is recieving fentanyl for her pain, a medicine to paralyze her and a sedative. During this time were told that a preliminary diagnosis of Pulmonary Interstitial Glyconesis had been determined based on her lung biospy. This rare lung disease has a good prognosis and case studies have shown that 5 day steroid treatment has shown to be effective in other children. Elizabeth was started on her 5 day treatment for the lung disease and she was also started on Sildenafil for the pulmonary hypertension. We were told that the Sildenfail would basically take the place of the nitric oxide, she should be able to wean off of the nitric once the max dose of Sildenafil was reached.